013. COPA syndrome - a new condition to consider when features of polyarthritis and interstitial lung disease are present
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چکیده
منابع مشابه
Bagpipe lung; a new type of interstitial lung disease?
To cite: King J, Richardson M, Quinn A-M, et al. Thorax Published Online First: [please include Day Month Year] doi:10.1136/thoraxjnl-2016208751 BACKGROUND Hypersensitivity pneumonitis (HP) is an inflammatory lung disease mediated by an immunological response to an inhaled antigen and can progress to disabling or fatal lung disease. It is related to occupational or other environmental exposures...
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Children interstitial lung (ChILD) disease is a large group of disorders with damage in alveolus and capillary. Although these disorders resemble ILD of adult in nomination, ChILD represents different pathologic and clinical patterns. A 2.5 months old girl, with failure to thrive and grunting and dyspnea, complained of staccato coughs without association with feeding, since she was 15 days o...
متن کاملAnti-KJ: a new antibody associated with the syndrome of polymyositis and interstitial lung disease.
Antibodies to aminoacyl-tRNA synthetases (anti-Jo-1, anti-PL-7, anti-PL-12) have been found in the serum of some patients with polymyositis (PM). Patients with these antibodies have an unusually high rate of interstitial lung disease (ILD) in association with their PM. Two patients (K.J. and B.T.) with severe ILD and PM were found to have antibodies to a cytoplasmic antigen, but tests to determ...
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Hermansky-Pudlak syndrome is a rare disease characterized by bleeding diathesis, oculocutaneous albinism and lysosomal ceroid lipofuscin pigment deposits. Pulmonary fibrosis may also accompany with the disease. A 48-year-old male patient with a diagnosis of Hermansky-Pudlak syndrome admitted with dyspnea. A thorax computed tomography revealed bilateral diffuse interlobular septal thickness whic...
متن کاملIgG4-related interstitial lung disease: a new and evolving concept.
PURPOSE OF REVIEW This review examines recent advances in our knowledge of the clinical, pathological, diagnostic, and therapeutic aspects of IgG4-related interstitial lung disease (ILD). RECENT FINDINGS A recent case series of ILD with IgG4-positive plasma cells suggested grade 1 lymphomatoid granulomatosis. The presence of the IgG4-positive plasma cells with the lack of atypical cells favor...
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ژورنال
عنوان ژورنال: Rheumatology
سال: 2017
ISSN: 1462-0324,1462-0332
DOI: 10.1093/rheumatology/kex356.059